Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.

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Loss of lamina dura, decreased skull bone density, and sporadic bony defects all served as convincing evidence of the serious osseous fragility.

Expert curators review the literature and organize it to facilitate your work. We present an adolescent case with recurrent familial gigantiform cementoma who received surgical intervention in our hospital.

Familial gigantiform cementoma: classification and presentation of a large pedigree.

csmentoma Retrieved from ” https: A diagnosis of a gigantiform cementoma was made. Familial gigantiform cementoma with brittle bone disease, pathologic fractures and osteosarcoma: Topics Discussed in This Paper. Please review our privacy policy. InMoshref et al 8 again reported a FGC case series with frequent fracture history.

Gigantiform cementoma in a child

For the latest visit to our clinic 2 months ago, the cementma in the neomandible region was desirable, and in parallel, the recent DEA test result took a favorable turn as BMD had increased to Abstract The objective of this report is to present an unusual case of a gigantiform cementoma manifesting with gross expansion of the maxilla in a 6-year-old black female. This article has been cited by other articles in PMC.


Multiquadrant expansile fibro-osseous lesion in a juvenile. Genetically predisposing as FGC seems, emphasis of management has largely been confined to mostly afflicted maxillas and mandibles.

B Preoperative panorex X-ray showed a characteristic radiographic feature of familial gigantiform cementoma FGC with well-circumscribed radiopaque areas involving all quadrants of the jaw, with mandible being more severely damaged. Gigantifrom radiographic changes and related bone metabolism disorder are herein hypothesized and discussed. B Reconstructed computed tomography image of familial gigantiform cementoma appearance.

Classification and presentation of a large pedigree. Ogunsalu CO, Miles D.

Familial Gigantiform Cementoma

This article has been cited by other articles in PMC. Therefore, we present a case with a large FGC family history so as to sketch a more detailed portrait of such ailment.

Cementomma Syndrome — the importance of early diagnosis: Infected lesions and those presenting with progressive expansion are generally removed surgically through enucleation. This article does not cite any sources. F 3-D computed tomography reconstruction of postoperative view. The giyantiform had an early age of onset and developed slowly.


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A possible explanation of an ancient mystery. We might not hastily come to the conclusion that coexistence of FGC and polyostotic pathologic fractures is mere coincidental clinical manifestation. A The adolescent patient with a huge mass extending along the mandible body.

Periprosthetic bone mineral density changes after unicondylar knee arthroplasty.

The growth of the disfigured mandible had not yet been deterred, but instead, accelerated, accompanied by teeth loss and altered dietary patterns. Gigantiform cementoma in a child.

In our patient the radiological, macroscopic and microscopic appearances are characteristics of a gigabtiform OD.